Café au lait spots are often harmless but may be associated with syndromes such as –
- Neurofibromatosis type 1
- McCune–Albright syndrome
Neurofibromatosis Type 1 –
- Café au lait lesions tend to resemble the “coast of California,” rather than the “coast of Maine,”
- Meaning the edges are smoother and more linear.
Café au lait lesions with rough borders (“coast of Maine”)